Esclerodermia y cirrosis biliar primaria (Síndrome de Reynolds): Descripción de un caso

Merly Montenegro-Polo, Carlos Llanos-Florez, Andrés Mier-Beleño, Sily Maestre-Zabala, Ronald Maestre Serrano, Carlos Barrera Guarín

Resumen


[Scleroderma and Primary Biliary Cirrhosis (Reynolds syndrome): Case Description]

RESUMEN:

El síndrome de Reynolds, se define como cirrosis biliar primaria en pacientes con esclerodermia; este sindrome debe ser sospechado en aquellos pacientes que desarrollen un patrón colestásico. Se reporta el caso de una paciente con antecedente de esclerodermia que consulta por cuadro de ictericia y a quien se le realiza estudios inmunológicos y confirmación histopatológica hepática con diagnóstico de cirrosis biliar primaria. Se ordena acido ursodesoxicólico 15mg/día por especialidades tratantes.

 

 

 

  ABSTRACT

Reynolds syndrome is defined as primary biliary cirrhosis in patients with scleroderma; this sindorme should be suspected in those patients who develop a cholestatic pattern. We report the case of a patient with a history of scleroderma who consulted due to jaundice and who underwent immunological studies and liver histopathological confirmation with a diagnosis of primary biliary cirrhosis. Ursodeoxycholic acid 15mg / day is ordered by treating specialties

 


 

 

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Referencias


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